Those who have Dravet syndrome, an uncommon and severe type of epilepsy, usually experience their first seizure inside the newbie of existence, based on the Epilepsy Foundation. (1)
These early seizures, that are typically triggered with a fever or contact with temperature changes, are often convulsive or involve jerking movements somewhere from the body.
Between ages 1 and 5, most kids with Dravet syndrome will start to have myoclonic seizures, which entail brief jerks of the muscle or muscle. However the disorder may also cause numerous other kinds of seizures too.
Dravet syndrome is because an inherited mutation, but it’s not often inherited from parents. There’s no remedy for the disorder, but treatment concentrates on lowering the severity and frequency of seizures and also the connected complications, particularly status epilepticus (when seizures don’t stop or occur close together), which may be existence-threatening.
Preventing Dravet Syndrome Seizures
The next triggers may cause seizures in those who have Dravet syndrome: (2)
Fevers, which needs to be given medications like ibuprofen (Advil) or acetaminophen (Tylenol)
Overheating (typically from hot baths or exercise)
Sudden temperature changes (cold or hot)
Visual stimuli like stripes along with other contrasting patterns
Stress or excessive excitement
Vaccines (your child’s doctor may counsel you to provide your son or daughter temperature reducer before a vaccination as well as for 24 hrs afterward to prevent temperature)
First-Line Drugs for Dravet Syndrome
In the start of Dravet syndrome, doctors may prescribe anticonvulsant medications like valproic acidity and clobazam to manage seizures, however they usually aren’t effective enough by themselves. (3)
There’s little research about how effective valproic acidity is perfect for handling the seizures connected with Dravet syndrome. However in some studies, about one-4th to 1-1 / 2 of study participants responded well towards the medication, experiencing greater than a 50 % decrease in the regularity of seizures. (4)
However, valproic acidity could cause several severe negative effects, including liver damage, elevated bloodstream ammonia, pancreatitis (inflammation from the pancreas), and occasional bloodstream platelet count. Less-severe negative effects include altered appetite, hair thinning, tremor, and sedation.